Primary spinal intradural extramedullary lymphoma causing cauda equina syndrome
Goutham Cugati1, Manish Singh, Nigel Peter Symss
1Department of Neurosurgery, Narayana Hrudayalaya Multispeciality Hospitals, Mysore, Karnataka, India.
Journal of Craniovertebral Junction & Spine
|October 2, 2013
Summary
A rare pediatric spinal lymphoma caused cauda equina syndrome in an 11-year-old boy. Surgical removal led to near-normal neurological function, highlighting effective management for this uncommon condition.
Area of Science:
- Neurology
- Pediatric Oncology
- Spinal Surgery
Background:
- Intradural extramedullary lesions are rare spinal tumors.
- Primary spinal lymphomas are exceptionally uncommon, particularly in children.
- Cauda equina syndrome requires prompt diagnosis and intervention.
Observation:
- An 11-year-old boy presented with cauda equina syndrome and acute bladder dysfunction.
- An intradural extramedullary lesion was identified in the lumbar spine.
- The lesion was surgically resected under emergency conditions.
Findings:
- Histopathology and immunohistochemistry confirmed the lesion as lymphoma.
- This represents the first pediatric case of primary spinal intradural extramedullary lymphoma causing cauda equina syndrome.
- The patient experienced significant neurological improvement post-surgery.
Implications:
- This case expands the understanding of rare spinal tumors in pediatric patients.
- Early surgical management can lead to favorable neurological outcomes.
- Further research into the pathogenesis and optimal treatment strategies for spinal lymphomas is warranted.
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