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Updated: May 7, 2026

Assays for the Degradation of Misfolded Proteins in Cells
Published on: August 28, 2016
Mitochondrial protein quality control in health and disease
Michael J Baker1, Catherine S Palmer, Diana Stojanovski
1Department of Biochemistry and Molecular Biology and Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Melbourne, VIC, Australia; ARC Centre of Excellence for Coherent X-ray Science, Melbourne, VIC, Australia.
Abstract:
Progressive mitochondrial dysfunction is linked with the onset of many age-related pathologies and neurological disorders. Mitochondrial damage can come in many forms and be induced by a variety of cellular insults. To preserve organelle function during biogenesis or times of stress, multiple surveillance systems work to ensure the persistence of a functional mitochondrial network. This review provides an overview of these processes, which collectively contribute to the maintenance of a healthy mitochondrial population, which is critical for cell physiology and survival.
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