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Catheter-based Endovascular Angioplasty for Fibrosing Mediastinitis-associated Pulmonary Vein Stenosis
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Papillary fibroelastoma of the pulmonary valve--a systematic review

Fayaz A Hakim1, Madan Raj Aryal, Anil Pandit

  • 1Division of Cardiovascular Diseases, Department of Medicine, Mayo Clinic, Scottsdale, Arizona.

Echocardiography (Mount Kisco, N.Y.)
|October 17, 2013
PubMed

Insights

Pulmonary valve papillary fibroelastomas (PVPFE) are rare benign tumors. This review details their demographics, presentation, and management, highlighting potential complications like obstruction and embolism.

Area of Science:

  • Cardiology
  • Cardiac Surgery
  • Oncology

Background:

  • Valvular papillary fibroelastomas are rare cardiac tumors.
  • The pulmonary valve is an uncommon site for these tumors.
  • Increased use of imaging has led to more frequent diagnoses.

Purpose of the Study:

  • To systematically review demographic characteristics of pulmonary valve papillary fibroelastomas (PVPFE).
  • To outline the clinical presentation, management strategies, and outcomes for PVPFE.
  • To address the rarity and potential complications of this benign pulmonary valve tumor.

Main Methods:

  • Systematic literature review.
  • Analysis of demographic data.
  • Evaluation of clinical presentations and management outcomes.

Main Results:

  • Pulmonary valve papillary fibroelastomas are infrequently diagnosed.
  • Shortness of breath is a common symptom in symptomatic patients.
  • Embolic events and right ventricular outflow tract obstruction are significant complications.

Conclusions:

  • Pulmonary valve papillary fibroelastomas require careful consideration due to potential serious complications.
  • Early recognition and appropriate management are crucial for favorable outcomes.
  • Further research is needed to fully understand the long-term prognosis of PVPFE.
Keywords:
papillary fibroelastomapulmonary valve

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