Unfused crossed renal ectopia with ipsilateral anorchia-a rare entity

The reported incidence of unfused crossed renal ectopia is 1 in 75,000 autopsies. A majority of such cases go unnoticed, as they remain asymptomatic and are found incidentally at autopsy. We have presented such a case for its rarity, unusual presentation and association, and have discussed it in light of the available literature. In this report, a 7-year-old boy was pre-operatively diagnosed as having left crossed renal ectopia with a cryptorchid left testis. At surgery, we noticed an ectopic, hydronephrotic left kidney with an absent left testis. Left Nephrectomy was performed, based on findings of a DTPA scan which was done. Post-operative course was uneventful. Histopathology revealed chronic pyelonephritis without any evidence of dysplastic changes.