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γ375W fibrinogen-synthesizing CHO cells indicate the accumulation of variant fibrinogen within endoplasmic reticulum

Tamaki Kobayashi1, Shinpei Arai2, Naoko Ogiwara3

  • 1Department of Clinical Laboratory Investigation, Shinshu University, Matsumoto, Japan.

Thrombosis Research
|November 12, 2013
PubMed

Keywords:
Endoplasmic reticulumFibrinogen storage diseaseFibrinogen γ-chain mutationHepatic endoplasmic reticulum storage diseaseHypofibrinogenemia

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