Modified abdominoplasty for patients with the Prune Belly syndrome

Francisco Tibor Dénes1, Roberto Iglesias Lopes1, Lorena Marçalo Oliveira1

  • 1Division of Urology, University of São Paulo Medical School, São Paulo, Brazil.

Urology
|November 16, 2013
PubMed

Insights

This study introduces a novel abdominoplasty technique for Prune Belly syndrome (PBS) patients, achieving excellent cosmetic and functional outcomes. The procedure effectively improves abdominal tonus and appearance in children with this rare congenital condition.

Area of Science:

  • Pediatric Surgery
  • Urology
  • Plastic Surgery

Background:

  • Prune Belly syndrome (PBS) is a rare congenital disorder characterized by abdominal muscle deficiency, urinary tract abnormalities, and cryptorchidism.
  • Abdominoplasty is a crucial component of surgical management for PBS, aiming to improve abdominal wall function and aesthetics.

Purpose of the Study:

  • To present the outcomes of a new abdominoplasty technique in pediatric patients diagnosed with Prune Belly syndrome.
  • To evaluate the safety, efficacy, and cosmetic results of this innovative surgical approach.

Main Methods:

  • A cohort of 46 children with PBS underwent surgical treatment including urinary tract reconstruction (UTR), orchidopexy, and abdominoplasty.
  • The described abdominoplasty technique involves specific steps for musculo-aponeurotic fascia (MAF) repair and skin closure, preserving the umbilicus.

Main Results:

  • Excellent skin coaptation was achieved in all 41 patients who underwent the new abdominoplasty technique, with no need for trimming or instances of dehiscence or skin necrosis.
  • Immediate improvement in abdominal tonus and appearance was observed, with further enhancement noted during growth in most patients.

Conclusions:

  • The presented abdominoplasty technique is effective and applicable across all forms of abdominal wall weakness associated with Prune Belly syndrome, including asymmetrical presentations.
  • The procedure yields favorable cosmetic and functional results, requiring only a single MAF incision.
Abstract