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Apical hypertrophic cardiomyopathy in association with pulmonary artery hypertension

Mehdi Peighambari1, Mozghan Parsaei, Anita Sadeghpour

  • 1Rajaie Cardiovascular Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran.

Journal of Cardiovascular and Thoracic Research
|November 20, 2013
PubMed

Insights

Apical Hypertrophic Cardiomyopathy (HCM) is rare. This study reports two cases of apical HCM associated with significant pulmonary artery hypertension, with no other identifiable cause.

Area of Science:

  • Cardiology
  • Pulmonology

Background:

  • Apical Hypertrophic Cardiomyopathy (HCM) is a distinct subtype of HCM, accounting for 1%-2% of all HCM diagnoses.
  • HCM is characterized by unexplained left ventricular hypertrophy.

Observation:

  • Two patients presented with apical HCM.
  • Both patients exhibited significant pulmonary artery hypertension.
  • No other underlying conditions were identified as a cause for the pulmonary hypertension.

Findings:

  • Echocardiography, cardiac catheterization, and pulmonary function tests were performed.
  • The findings suggest a potential association between apical HCM and unexplained pulmonary artery hypertension.

Implications:

  • This association may warrant further investigation into the pathophysiology linking apical HCM and pulmonary hypertension.
  • Understanding this relationship could lead to improved diagnostic and therapeutic strategies for patients with these co-occurring conditions.

Keywords:
Apical Hypertrophic CardiomyopathyEchocardiographyPulmonary Artery Hypertension

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