Dyke davidoff masson syndrome. A case report

Area of Science:

• Neurology
• Pediatrics
• Radiology

Background:

• Cerebral hemiatrophy, or hemiatrophy of one cerebral hemisphere, is a rare condition.
• Early-onset hemiatrophy (first two years of life) can lead to characteristic cranial changes.

Purpose of the Study:

• To describe a case of Dyke Davidoff Masson Syndrome (DDMS) in a pediatric patient.
• To highlight the clinical presentation and potential etiology of cerebral hemiatrophy.

Main Methods:

• Case report of a 12-year-old child.
• Clinical examination and diagnostic evaluation for neurological deficits.

Main Results:

• The patient presented with seizures, hemiplegia, and mental retardation.
• Features consistent with DDMS were observed, including cerebral hemiatrophy and contralateral paresis.
• Ipsilateral cranial changes such as skull hypertrophy and sinus hyper-pneumatization were noted.

Conclusions:

• Dyke Davidoff Masson Syndrome (DDMS) presents with cerebral hemiatrophy, neurological deficits, and associated cranial abnormalities.
• Vascular occlusion is a probable cause of hemiatrophy in early childhood.
• This case underscores the importance of recognizing DDMS in children with asymmetric neurological symptoms.