Congenital Heart Defects in Adults : A Field Guide for Cardiologists

Anitra Romfh1, Francesca Romana Pluchinotta, Prashob Porayette

  • 1Department of Cardiology, Children's Hospital Boston, Boston, MA 02115, USA ; Division of Cardiovascular Medicine, Department of Medicine, Brigham and Women's Hospital, Boston, MA 02115, USA.

Journal of Clinical & Experimental Cardiology
|December 3, 2013
PubMed

Insights

Adult congenital heart disease requires specialized knowledge. This guide overviews common defects, their complications, and management for adult cardiologists caring for survivors of congenital heart defects.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Adult Cardiology

Background:

  • Advances in cardiology and cardiac surgery enable more congenital heart defect (CHD) patients to reach adulthood.
  • Adult CHD patients often develop unique complications related to their defect or treatment.
  • Adult cardiologists require updated knowledge on common CHDs presenting in adulthood.

Purpose of the Study:

  • To provide adult cardiologists with a working knowledge of common congenital heart defects.
  • To serve as a field guide for managing adult patients with CHDs.
  • To detail anatomy, physiology, clinical presentation, complications, and outcomes of selected CHDs.

Main Methods:

  • Overview of selected CHD anatomy using pathology specimens.
  • Inclusion of clinical imaging studies for anatomical visualization.
  • Description of physiology, clinical presentation, complications, treatment, and outcomes.

Main Results:

  • Detailed anatomical review of common adult CHD using specimens and imaging.
  • Explanation of physiological changes and clinical presentations in adults.
  • Summary of potential complications, treatment strategies, and patient outcomes.

Conclusions:

  • Adult cardiologists must be knowledgeable about common CHDs for effective patient care.
  • This guide aids in understanding and managing adult patients with congenital heart disease.
  • Comprehensive knowledge of CHD anatomy, physiology, and management is crucial for improved outcomes.

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