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Bazex syndrome
Ismael Alves Rodrigues1, Letícia Trivellato Gresta1, Rafaela Carolina Cruz2
1Federal University of Minas Gerais.
Anais Brasileiros De Dermatologia
|December 19, 2013
Summary
Acrokeratosis Paraneoplastica, a rare skin condition, often signals squamous cell carcinoma. This case highlights its typical lesions in a patient with esophageal cancer.
Area of Science:
- Dermatology
- Oncology
Background:
- Acrokeratosis Paraneoplastica, also known as Bazex syndrome, is a paraneoplastic dermatosis.
- It is most commonly associated with squamous cell carcinoma of the upper aerodigestive tract.
Observation:
- This report details a rare case of Acrokeratosis Paraneoplastica.
- The patient presented with exuberant and typical cutaneous lesions characteristic of the syndrome.
Findings:
- The patient was diagnosed with squamous cell carcinoma of the esophagus.
- This case underscores the association between Acrokeratosis Paraneoplastica and esophageal cancer.
Implications:
- Early recognition of Bazex syndrome's cutaneous manifestations can aid in the early diagnosis of underlying squamous cell carcinoma.
- This case expands the understanding of paraneoplastic syndromes involving the skin and internal malignancies.
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