Omphalomesenteric duct cyst in an omphalocele: a rare association

Yousuf Aziz Khan1, Mumtaz Ahmed Qureshi2, Jamshed Akhtar3

  • 1Yousuf Aziz Khan, MBBS, FCPS (Paediatric Surgeon), Department of Paediatric Surgery, National Institute of Child Health, Rafiquee Shaheed Road, Karachi - 75510, Sind, Pakistan.

Insights

Omphalomesenteric duct (OMD) remnants can occur with omphalocele in infants. This case highlights a rare OMD remnant presenting as a cyst, requiring surgical intervention.

Area of Science:

  • Pediatric Surgery
  • Developmental Biology
  • Gastrointestinal Surgery

Background:

  • Omphalomesenteric duct (OMD) remnants are congenital anomalies often associated with omphalocele in neonates.
  • Meckel's diverticulum is the most common OMD remnant found in omphalocele cases.
  • Rarely, other OMD-related lesions can present within an omphalocele sac.

Observation:

  • A one-day-old male infant presented with an omphalocele.
  • Surgical exploration revealed a 10 x 12 cm cyst containing intestinal contents as the omphalocele content.
  • The cyst was continuous with proximal and distal ileal loops.

Findings:

  • The cyst was surgically resected, followed by primary intestinal anastomosis.
  • The infant also had complex cardiac anomalies.
  • The infant succumbed to sepsis a few days post-operatively.

Implications:

  • This case underscores the importance of thorough surgical exploration for omphaloceles to identify unusual OMD remnants.
  • Management requires prompt surgical intervention for OMD remnants and omphalocele.
  • Associated congenital anomalies, such as cardiac defects, can significantly impact patient outcomes.

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