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Published on: February 11, 2022
Cor triatriatum sinister in a 43-year-old man with syncope
Janet L Eichholz1, Samer S Hodroge1, Jerry J Crook1
1Departments of Cardiology (Drs. Crook, Eichholz, and Wortham), Internal Medicine (Dr. Hodroge), and Cardiothoracic Surgery (Dr. Mack), The University of Tennessee Medical Center, Knoxville, Tennessee 37920.
Insights
Cor triatriatum sinister, a rare congenital heart defect, involves a membrane dividing the left atrium. This case highlights a rare adult presentation diagnosed via syncope, successfully treated with membrane resection.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Cor triatriatum sinister is a rare congenital cardiac anomaly where a fibromuscular membrane partitions the left atrium.
- It affects 0.1% to 0.4% of patients with congenital heart disease, typically diagnosed in infancy or childhood.
- Adult presentations are uncommon, often presenting with atypical symptoms.
Observation:
- A 43-year-old male presented with recurrent syncope as his sole symptom.
- Diagnostic workup revealed cor triatriatum sinister, a rare congenital heart anomaly.
- The patient's symptoms were attributed to the left atrial partitioning by the fibromuscular membrane.
Findings:
- Surgical resection of the dividing membrane was performed.
- The patient experienced complete symptom resolution following the corrective procedure.
- This case underscores the potential for late diagnosis and successful surgical intervention in adult cor triatriatum sinister.
Implications:
- Highlights the importance of considering rare congenital heart anomalies in adult syncope evaluations.
- Demonstrates the efficacy of surgical correction for cor triatriatum sinister in adult patients.
- Contributes to the literature on adult-onset congenital cardiac defects and their management.
Abstract:
Cor triatriatum sinister, a congenital cardiac anomaly involving a fibromuscular membrane that partitions the left atrium into 2 chambers, has been reported in only 0.1% to 0.4% of patients with congenital heart disease. The posterosuperior chamber receives blood from the pulmonary veins, and the anteroinferior chamber contains the left atrial appendage and mitral valve orifice. Most patients are diagnosed with the condition in infancy or childhood; adult cases are rare. We describe a case of cor triatriatum sinister in a 43-year-old man whose only presenting symptom was recurrent syncope. He underwent corrective resection of the membrane and was asymptomatic thereafter. In addition to discussing the patient's case, we review the relevant medical literature.
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