Cor triatriatum sinister in a 43-year-old man with syncope

Janet L Eichholz1, Samer S Hodroge1, Jerry J Crook1

  • 1Departments of Cardiology (Drs. Crook, Eichholz, and Wortham), Internal Medicine (Dr. Hodroge), and Cardiothoracic Surgery (Dr. Mack), The University of Tennessee Medical Center, Knoxville, Tennessee 37920.

Insights

Cor triatriatum sinister, a rare congenital heart defect, involves a membrane dividing the left atrium. This case highlights a rare adult presentation diagnosed via syncope, successfully treated with membrane resection.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Cardiac Surgery

Background:

  • Cor triatriatum sinister is a rare congenital cardiac anomaly where a fibromuscular membrane partitions the left atrium.
  • It affects 0.1% to 0.4% of patients with congenital heart disease, typically diagnosed in infancy or childhood.
  • Adult presentations are uncommon, often presenting with atypical symptoms.

Observation:

  • A 43-year-old male presented with recurrent syncope as his sole symptom.
  • Diagnostic workup revealed cor triatriatum sinister, a rare congenital heart anomaly.
  • The patient's symptoms were attributed to the left atrial partitioning by the fibromuscular membrane.

Findings:

  • Surgical resection of the dividing membrane was performed.
  • The patient experienced complete symptom resolution following the corrective procedure.
  • This case underscores the potential for late diagnosis and successful surgical intervention in adult cor triatriatum sinister.

Implications:

  • Highlights the importance of considering rare congenital heart anomalies in adult syncope evaluations.
  • Demonstrates the efficacy of surgical correction for cor triatriatum sinister in adult patients.
  • Contributes to the literature on adult-onset congenital cardiac defects and their management.

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