Percutaneous coronary intervention in a 3-year-old with hypoplastic left heart syndrome

P M E Noonan1, D Taliotis1, A Alahmar1

  • 1East Midlands Congenital Heart Centre Glenfield Hospital, Groby Road, Leicester LE3 9QP.

Insights

This case report highlights a rare myocardial infarction in a child with hypoplastic left heart syndrome (HLHS). Thrombus aspiration successfully treated the coronary artery occlusion, improving clinical response.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Interventional Cardiology

Background:

  • Surgical palliation for hypoplastic left heart syndrome (HLHS) has improved, but interstage mortality remains a challenge.
  • Predicting and preventing interstage mortality in HLHS patients is crucial for better outcomes.

Observation:

  • A 3-year-old boy with HLHS, palliated with a Glenn shunt, presented with acute myocardial infarction.
  • The infarction was caused by near-total occlusion of the distal right coronary artery.

Findings:

  • The patient was successfully treated with thrombus aspiration, showing a good clinical response.
  • This is the first reported case of thrombus aspiration in complex pediatric congenital heart disease.

Implications:

  • Thrombus aspiration can be an effective treatment for acute coronary artery occlusion in pediatric congenital heart disease.
  • Collaboration between congenital and adult cardiologists is valuable for managing complex pediatric cardiac cases.

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