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Author Spotlight: Advancing Spectral Characterization of Physiological and Malperfused Tissues
Published on: July 5, 2024
Vena caval anomalies
Ramyah Rajakulasingam1, Rohin Francis2, Ramanan Rajakulasingam2
1Department of Cardiology, East and North Hertfordshire NHS Trust, United Kingdom ; Lister Hospital, East and North Hertfordshire NHS Trust, United Kingdom.
Insights
This case report details a rare combination of congenital heart anomalies: a bicuspid aortic valve, persistent left superior vena cava, and a left-sided inferior vena cava. Understanding these venous anomalies is vital for cardiac procedures.
Area of Science:
- Cardiology
- Anatomical Pathology
- Medical Imaging
Background:
- Anomalous venous anatomy, particularly involving the superior and inferior vena cava, can complicate cardiac interventions.
- Congenital heart defects such as bicuspid aortic valve are relatively common.
- The persistent left superior vena cava (PLSVC) is the most common congenital anomaly of the superior vena cava.
Observation:
- A 44-year-old female presented with a rare constellation of cardiovascular anomalies.
- She possessed a bicuspid aortic valve.
- Additionally, she had a persistent left superior vena cava draining into the coronary sinus and a left-sided inferior vena cava that connected via the hemiazygos vein to the PLSVC.
Findings:
- This case represents the first reported instance of an association between bicuspid aortic valve, PLSVC with coronary sinus drainage, and a left-sided IVC draining into the PLSVC.
- Detailed imaging confirmed the complex venous drainage pattern.
Implications:
- Accurate identification of anomalous vena cavae is critical for the safety and success of right-sided heart procedures.
- Awareness of such combined anomalies is essential for interventional cardiologists and cardiac surgeons.
- This case highlights the importance of thorough pre-procedural anatomical assessment in patients with congenital heart disease.
Abstract:
Anomalous vena cavae can have significant implications for procedures on the right side of the heart. We report a rare anatomical configuration in a 44-year-old female, which to the best of our knowledge, is the first report of such an association. She had a bicuspid aortic valve in conjunction with a persistent left superior vena cava (PLSVC) draining into the coronary sinus, and a left-sided inferior vena cava (IVC) draining into a left superior vena cava via the hemiazygos vein. Comprehensive assessment of these anomalies is crucial given the widespread use of invasive cardiac procedures.
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