Dysgenesis of the inferior vena cava associated with deep venous thrombosis and a partial Protein C deficiency

Howard Tribe1, Rudi Borgstein1

  • 1Department of Radiology, North Middlesex Hospital, London, UK.

Insights

Inferior vena cava dysgenesis, a rare condition, can present atypically in children with deep venous thrombosis. Early advanced imaging is crucial for diagnosis and treatment of this congenital abnormality.

Area of Science:

  • Vascular Surgery
  • Pediatric Radiology
  • Hematology

Background:

  • Inferior vena cava (IVC) dysgenesis is a rare congenital anomaly.
  • It is increasingly diagnosed with advanced cross-sectional imaging.
  • Patients are often asymptomatic, with incidental findings.

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