Gingival fibrinoid deposits in Ehlers-Danlos syndrome

A 7-year-old girl is described with Ehlers-Danlos syndrome Type VIII. Symptoms mainly consisted of rapid breakdown of the periodontal tissues. The gingiva exhibited the presence of peculiar previously unidentified cell-poor masses resembling fibrin by their staining properties. Possibly, this histologic feature may be a diagnostic aid in Ehlers-Danlos syndrome Type VIII.