Angiokeratoma circumscriptum in a young male

Area of Science:

• Dermatology
• Vascular Malformations
• Neoplastic Disease

Background:

• Angiokeratomas are vascular ectasias of the papillary dermis.
• Angiokeratoma circumscriptum (AKC) is the rarest variant, typically showing female predominance.
• AKC is an extremely rare nevoid disorder with limited reported cases.

Purpose of the Study:

• To report a case of angiokeratoma circumscriptum in a young male.
• To highlight diagnostic challenges and the importance of accurate counseling.
• To present a successful treatment outcome for AKC.

Main Methods:

• Clinical examination of a 20-year-old male with congenital leg lesions.
• Histopathological analysis confirming hyperkeratosis, acanthosis, and vascular proliferation.
• Surgical excision and skin grafting for treatment.

Main Results:

• The patient presented with painful, verrucous linear plaques on the right leg.
• Histopathology confirmed angiokeratoma circumscriptum.
• Excision and skin grafting resulted in a cosmetically favorable outcome.

Conclusions:

• Angiokeratoma circumscriptum can occur in males, contrary to its typical female preponderance.
• Accurate diagnosis and appropriate counseling are crucial for managing AKC.
• Surgical intervention can achieve favorable cosmetic results for AKC.