Bilateral single system ectopic ureters opening into vestibule with bladder agenesis

Area of Science:

• Urology
• Pediatric Urology
• Congenital Anomalies

Background:

• Ectopic ureters, often associated with duplicated systems (80%) and occurring bilaterally (5-17%), typically drain into the urethra, vestibule, vagina (females), or posterior urethra and seminal vesicles (males).
• Bilateral single-system ectopic ureter (BSSEU) represents a rare congenital anomaly within urological practice.

Observation:

• This report details an exceptionally rare case of BSSEU presenting with an opening into the vestibule.
• A critical and highly unusual feature of this case is the complete absence of a urinary bladder.

Findings:

• The study identifies and describes an extremely rare urological condition: bilateral single-system ectopic ureter opening into the vestibule without a urinary bladder.
• Management strategies for this unique presentation are briefly discussed.

Implications:

• This case expands the known spectrum of congenital urinary tract malformations.
• Understanding and managing such rare anomalies is crucial for improving patient outcomes in pediatric urology.
• Highlights the importance of thorough diagnostic evaluation for complex ectopic ureter presentations.