One-stage surgical correction in pentalogy of Cantrell with left ventricular diverticulum
Yang Liu1, Jian Yang, Zhenxiao Jin
1Department of Cardiac Surgery, Xijing Hospital Forth Military Medical University, Xi'an, Shaanxi, China.
Insights
Pentalogy of Cantrell, a rare congenital malformation, often includes a left ventricular diverticulum. Simultaneous surgical correction of intracardiac defects and diverticulum offers favorable short-term outcomes in selected patients.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Surgical Innovation
Background:
- Pentalogy of Cantrell is a rare, complex congenital malformation with high mortality.
- Left ventricular diverticulum is a frequent component of this syndrome.
- Effective management strategies are crucial for improving patient survival.
Observation:
- This report details the surgical experience with three pediatric patients diagnosed with Pentalogy of Cantrell.
- All three patients presented with an associated left ventricular diverticulum.
- Surgical intervention focused on simultaneous correction of intracardiac anomalies and the diverticulum.
Findings:
- One-stage surgical correction was performed for both intracardiac malformations and left ventricular diverticulum.
- All three patients experienced uneventful recoveries following the simultaneous surgical approach.
- This approach demonstrated positive short-term outcomes in the presented cases.
Implications:
- Simultaneous one-stage surgical correction may be a viable and effective strategy for Pentalogy of Cantrell.
- This approach could potentially improve the short-term prognosis for selected pediatric patients.
- Further research into long-term outcomes of this surgical technique is warranted.
Abstract:
The pentalogy of Cantrell is a rare and fatal malformation. A left ventricular diverticulum is a common finding of this pentalogy. The present report summarizes our experience with three patients who suffered from pentalogy of Cantrell. All three cases had a left ventricular diverticulum. The intracardiac malformations and the left ventricular diverticulum were corrected simultaneously. All patients recovered uneventfully. One-stage surgical correction could improve short-term outcomes in selected patients with pentalogy of Cantrell.
