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06:20
Murine Bilateral Renal Lymphadenectomy
Published on: December 30, 2025
214
Tuberous sclerosis with bilateral renal angiomyolipoma
The Journal of the Association of Physicians of India
|March 20, 2014
Summary
Tuberous sclerosis, the second most common neurocutaneous syndrome, can present with rare bilateral renal angiomyolipomas. This report details two such cases, highlighting this uncommon manifestation.
Area of Science:
- Medical Science
- Genetics
- Nephrology
Background:
- Tuberous sclerosis is a genetic disorder affecting multiple organs.
- Neurocutaneous syndromes are a group of disorders affecting the brain, spinal cord, and skin.
- Renal angiomyolipomas are benign tumors that grow in the kidneys.
Observation:
- Bilateral renal angiomyolipomas are a rare complication of tuberous sclerosis.
- Two cases of tuberous sclerosis with bilateral renal angiomyolipomas were identified.
Findings:
- The study reports on two patients diagnosed with tuberous sclerosis.
- Both patients presented with bilateral renal angiomyolipomas, a rare occurrence.
- This finding underscores the importance of monitoring for renal complications in tuberous sclerosis patients.
Implications:
- Early detection and management of renal angiomyolipomas in tuberous sclerosis patients are crucial.
- Further research may elucidate the specific mechanisms leading to bilateral renal involvement.
- This case series contributes to the understanding of tuberous sclerosis spectrum of renal disease.
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