Positional oximetry to screen for pulmonary arteriovenous malformations in HHT
Susan Carpenter1, Janina Josepovici1, Giuseppe Latino1
1Division of Respiratory Medicine, Department of Paediatrics, The Hospital for Sick Children, Toronto, Canada.
Thorax
|April 8, 2014
Abstract:
Orthodeoxia has been described in patients with hereditary haemorrhagic telangiectasia (HHT) and pulmonary arteriovenous malformations (PAVM), but its usefulness in screening children for PAVMs is unknown. We show here that while oximetry is overall lower in children with significant PAVMs, supine and upright oximetry is of no additional diagnostic value indicating that positional oximetry is not a useful screening test for PAVMs.
Keywords:
Rare lung diseases

