Related Experiment Video

Updated: May 1, 2026

Repeated Measurement of Respiratory Muscle Activity and Ventilation in Mouse Models of Neuromuscular Disease
09:24

Repeated Measurement of Respiratory Muscle Activity and Ventilation in Mouse Models of Neuromuscular Disease

Published on: April 17, 2017

12.9K

[Neuromuscular disease: respiratory clinical assessment and follow-up]

C Martínez Carrasco1, J R Villa Asensi2, M C Luna Paredes3

  • 1Sección de Neumología Pediátrica, Hospital Universitario La Paz, Madrid, España.

Anales De Pediatria (Barcelona, Spain : 2003)
|April 9, 2014
PubMed

Insights

Patients with neuromuscular diseases face high risks of respiratory failure. Early specialist care, including ventilatory and cough support, significantly improves their quality of life and survival rates.

Area of Science:

  • Neurology
  • Pulmonology
  • Pediatrics

Context:

  • Neuromuscular diseases (NMDs) pose significant risks for pediatric patients, often leading to respiratory failure.
  • Effective management requires specialized pediatric respiratory medicine follow-up from diagnosis.
  • Multidisciplinary care is crucial for addressing respiratory complications in NMDs.

Purpose:

  • To review the pathophysiology, respiratory function, sleep disorders, and common respiratory complications in pediatric NMDs.
  • To highlight the importance of specialized respiratory care for NMD patients.
  • To provide a foundation for understanding respiratory management strategies in NMDs.

Summary:

  • Neuromuscular diseases frequently cause respiratory failure, a primary cause of mortality in affected children.
  • Specialized pediatric respiratory care, including ventilatory support and cough assistance, enhances survival and quality of life.
  • This review covers NMD pathophysiology, respiratory evaluation, sleep issues, and frequent complications.

Impact:

  • Improved understanding of respiratory challenges in pediatric NMDs.
  • Emphasizes the critical role of early and specialized respiratory intervention.
  • Informs clinical practice for better patient outcomes and long-term survival.

Keywords:
Atrofia muscular espinalChronic respiratory failureDistrofia muscular de DuchenneDuchenne muscular dystrophyEnfermedad neuromuscularInsuficiencia respiratoria crónicaNeumología pediátricaNeuromuscular diseaseNon-invasive ventilationPediatric respiratory medicineSleep-disordered breathingSpinal muscular atrophyTrastorno respiratorio del sueñoVentilación no invasiva

More Related Videos

Evaluation of Respiratory Muscle Activation Using Respiratory Motor Control Assessment RMCA in Individuals with Chronic Spinal Cord Injury09:37

Evaluation of Respiratory Muscle Activation Using Respiratory Motor Control Assessment RMCA in Individuals with Chronic Spinal Cord Injury

Published on: July 19, 2013

9.7K
Functional and Morphological Assessment of Diaphragm Innervation by Phrenic Motor Neurons09:43

Functional and Morphological Assessment of Diaphragm Innervation by Phrenic Motor Neurons

Published on: May 25, 2015

17.3K

Related Concept Videos

Respiratory Assessment: Purpose and Indications01:19

Respiratory Assessment: Purpose and Indications

Respiratory assessment is a cornerstone of nursing assessments, crucial for the early detection of patient deterioration. This evaluation transcends routine procedures, representing a critical skill nurses must master to ensure optimal patient care.
Objectives and Importance:
The primary goal of respiratory assessment is to evaluate patients at early risk of clinical deterioration. Since respiratory distress often precedes other signs of declining health, breathing patterns and sounds become a...
2.1K
Assessment of Airway, Skin Color, and Use of Accessory Muscles01:30

Assessment of Airway, Skin Color, and Use of Accessory Muscles

A thorough assessment of respiratory health is paramount in clinical settings to identify and manage respiratory distress and ensure adequate oxygenation. This article elaborates on the critical aspects of respiratory evaluation, including airway assessment, skin color examination, and the observation of accessory muscle use, which are integral to effectively diagnosing and managing patients with respiratory conditions.
Introduction
The initial evaluation of a patient's respiratory system...
1.8K
Physical Assessment of the Respiratory Tract II: Inspection01:27

Physical Assessment of the Respiratory Tract II: Inspection

Physical assessment of the respiratory tract through inspection is a crucial step in understanding the patient's respiratory health. It provides insights into the functioning of the respiratory system, the musculoskeletal structure, and even the patient's nutritional status. This comprehensive approach involves observing several vital aspects: chest configuration, breathing patterns, respiratory rates, skin color, and use of accessory muscles.
Chest Configuration
The chest configuration...
1.4K
Assessment of Respiration01:23

Assessment of Respiration

The respiratory system's basic structures and primary functions lay the foundation for nurses' comprehensive respiratory assessments. This assessment includes subjective and objective data to gauge the patient's respiratory health.
Subjective Assessment: Nurses interview the patient to gather information directly during the subjective assessment. It includes questions about the individual's medical history, medications, and symptoms, focusing on past respiratory conditions like...
2.3K
Pneumonia III: Complications and Assessment01:30

Pneumonia III: Complications and Assessment

Pneumonia poses the potential for numerous complications that warrant consideration. These complications include the following:
1.4K
Respiratory System Abnormal Finding II: Palpation and Auscultation01:31

Respiratory System Abnormal Finding II: Palpation and Auscultation

In assessing respiratory abnormalities, palpation and auscultation are critical tools for detecting and interpreting various pathophysiological changes. These techniques provide insight into underlying disorders by evaluating tactile sensations and sounds produced by the respiratory system.
Palpation Findings
During a respiratory assessment, palpation can reveal several vital abnormalities:
2.1K