[Primary cardiac angiosarcoma in the right atrium with cardiac tamponade]

Primary cardiac angiosarcoma is very rare with an incidence of 0.0017∼0.19% in collected autopsy series, and its prognosis has been reported as being extremely poor( average survival of 6∼9 months). A 56-year-old man was referred to our hospital with cardiac tamponade caused by right atrial angiosarcoma, after initially being misdiagnosed as acute type A dissection. Echocardiography and chest computed tomography (CT) revealed a pedunculated tumor with a broad base which was originating from the right atrial wall and extended into atrio-ventricular (AV) groove. The tumor was completely resected, and a bovine pericardium patch was used for cardiac reconstruction. Histological examination showed angiosarcoma and a sign of radical excision. The patient, who made an uneventful recovery,was given postoperative radiotherapy and chemotherapy. He died of multiple systemic metastases 14 months postoperatively despite of multidisciplinary treatment. We discuss the therapeutic strategies available for this highly malignant cardiac tumor.