Related Experiment Video
Updated: May 1, 2026

Multifocal Electroretinograms
Published on: December 4, 2011
Homonymous hemianopia due to Erdheim-Chester disease
William L Hills1, Ahmad H Nassef, Marjorie R Grafe
1Department of Neuro-Ophthalmology (WLH, JF), Casey Eye Institute, Oregon Health & Science University, Portland, Oregon; Departments of Neurology (WLH) and Ophthalmology (WLH, JF), Oregon Health & Science University, Portland, Oregon; Arab Organization for Industrialization Hospital (AN), Cairo, Egypt; Department of Neuropathology (MRG), Oregon Health & Science University, Portland, Oregon; University of Pennsylvania School of Medicine (SJM), Philadelphia, Pennsylvania; Department of Radiology, Ophthalmology, and Otolaryngology (JLW), Oregon Health & Science University, Portland, Oregon; Department of Pathology (SKM, MTC), Thomas Jefferson University School of Medicine, Philadelphia, Pennsylvania; Department of Neuro-Ophthalmology (MLM), Wills Eye Institute, Philadelphia, Pennsylvania; and Departments of Neurology (MLM) and Ophthalmology (MLM), Thomas Jefferson University School of Medicine, Philadelphia, Pennsylvania.
Abstract:
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis typically affecting multiple organ systems. We report 2 patients who presented with homonymous hemianopia and were ultimately diagnosed with biopsy-confirmed ECD. We review the spectrum of ECD and its treatment as well as histopathological and immunohistochemical differentiation from other histiocytic disorders.
More Related Videos
Related Concept Videos
Photoreceptors and Visual Pathways
Visual Agnosia
Prosopagnosia
Focusing of Light in the Eye

