A case of idiopathic encephalomeningocele
Athanasios K Petridis1, Alexandros Doukas1, Hubertus M Mehdorn1
1Department of Neurosurgery, University Hospital of Schleswig-Holstein, Campus Kiel, Germany.
Insights
This case study details an adult temporobasal encephalomeningocele, a rare condition typically seen in children. Surgical removal successfully resolved the patient's chronic headaches.
Area of Science:
- Neurosurgery
- Neurology
- Congenital Abnormalities
Background:
- Encephalomeningocele, a neural tube defect, predominantly affects children, causing facial disfigurement.
- Adult cases are rare, often presenting with rhinorrhea, but this case highlights an atypical presentation.
- The etiology is typically a congenital cranial base fusion defect, though not apparent in this patient.
Purpose of the Study:
- To report a rare case of temporobasal encephalomeningocele in an adult female.
- To describe the diagnostic process and successful surgical management of this condition in an elderly patient.
- To highlight the varied clinical presentations of encephalomeningocele in adults.
Main Methods:
- Diagnostic imaging included brain magnetic resonance imaging (MRI), cranial computed tomography (CT), and MR cisternography.
- Surgical intervention involved a pterional approach for complete removal of the encephalomeningocele.
- Clinical assessment of symptoms, particularly headaches and rhinorrhea, was performed pre- and post-operatively.
Main Results:
- A 72-year-old female presented with chronic headaches, lacking typical symptoms like rhinorrhea.
- Imaging confirmed a temporobasal encephalomeningocele.
- Complete surgical excision of the lesion was achieved.
- The patient's headaches resolved completely following surgery.
Conclusions:
- Temporobasal encephalomeningocele can occur in adults without apparent congenital causes and may present atypically with headaches as the primary symptom.
- Advanced imaging techniques are crucial for diagnosing such rare conditions.
- Surgical intervention offers a definitive treatment, leading to symptom resolution.
Abstract:
In the present case we report about an encephalomeningocele in an adult female. Since the cause of this medical entity is a congenital fusion defect of the neural tube of the cranial base, most of the encephaloceles occurs in children leading to facial disfigurement. In the rare cases described in adults, rhinorrhea is usually present. Here we present a case of temporobasal encephalomeningocele in a 72-year-old female patient suffering from headaches in the last 4-5 years. No rhinorrhea or other significant neurological symptoms were noticed. No congenital cause was apparent. After diagnostic steps including brain magnetic resonance imaging (MRI), cranial computed tomography (CT) and MR cisternography, an encephalomeningocele was diagnosed. Through a pterional approach this was completely removed. The only symptom the patient complaint about, headache, was eliminated after surgery.
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