Case for diagnosis. Dermatofibrosarcoma protuberans.

Area of Science:

• Dermatopathology
• Surgical Oncology

Background:

• Dermatofibrosarcoma protuberans (DFSP) is a rare fibrohistiocytic tumor.
• It exhibits aggressive local growth and high recurrence rates, with low metastatic potential.

Observation:

• DFSP typically presents as a hardened plaque with nodule development.
• It predominantly affects the trunk, with acral locations being unusual.
• Histopathology shows spindle cells in a storiform pattern, positive for CD34.

Findings:

• The case presented involved a long-term evolution of DFSP in an unusual location.
• The tumor relapsed following initial surgical intervention.

Implications:

• This case underscores the importance of early diagnosis for DFSP.
• Appropriate surgical management is essential to reduce recurrence and avoid extensive resections with increased morbidity.