[Pulmonary Langerhans cell histiocytosis: report of a case]

Pulmonary Langerhans cell histiocytosis is a rare disease of young adults, usually smokers, which is associated with significant morbidity. The course of the disease is unpredictable, ranging from benign self-limiting types with spontaneous regression, to malignant forms with progression to respiratory failure and death. Its cause is unknown, but most authors believe that there is an alteration in immune system regulation in these patients. We report a case of a patient with the diagnosis of pulmonary Langerhans cell histiocytosis and review the clinical characteristics, diagnosis and treatment of this disease. We consider this case of interest due by the low frequency of this disease.