[Refractory status epilepticus presenting as shaken baby syndrome]

Andrea Fernandez-Menendez1, Raquel Buenache-Espartosa, Ana Coca-Perez

  • 1Hospital Universitario Ramon y Cajal, 28034 Madrid, Espana.

Revista De Neurologia
|June 11, 2014
PubMed

Insights

Infants experiencing convulsive status with fever may have shaken baby syndrome (SBS). Medical professionals should consider SBS in infants under six months with unexplained febrile seizures and signs of hemorrhage.

Area of Science:

  • Pediatrics
  • Neurology
  • Forensic Medicine

Background:

  • Convulsive status in infants often stems from febrile illnesses or central nervous system infections.
  • Shaken baby syndrome (SBS) presents with specific signs like bilateral hemorrhages and encephalopathy, particularly in infants under one year.
  • Febrile syndromes and conditions causing increased crying can precipitate infant shaking.

Observation:

  • Two infant cases presented with status epilepticus during a febrile syndrome.
  • Imaging revealed bilateral subdural hematomas in varying stages of development.
  • Ophthalmic examination showed bilateral retinal hemorrhages in both infants.

Findings:

  • The presented cases highlight a correlation between febrile illness, status epilepticus, and signs consistent with shaken baby syndrome.
  • Bilateral subdural and retinal hemorrhages are critical indicators in diagnosing SBS in infants with seizures.
  • Early recognition of SBS is crucial, especially in infants under six months experiencing febrile seizures.

Implications:

  • Clinicians should consider shaken baby syndrome in infants presenting with convulsive status, even with seemingly common febrile illnesses.
  • Prompt diagnosis and intervention for SBS can mitigate severe neurological damage and improve outcomes.
  • This underscores the importance of a high index of suspicion for non-accidental trauma in infants with unexplained neurological events.
Abstract

Related Concept Videos

Seizures l: Introduction01:20

Seizures l: Introduction

Understanding seizures and epilepsy relies on key definitions that help in recognizing, classifying, and managing these disorders. These definitions provide a framework for recognizing, classifying, and managing seizure disorders.DefinitionsA seizure is a sudden, abnormal burst of electrical activity in the brain that can cause changes in awareness, movement, sensation, or behavior, depending on the area involved. Epilepsy is a chronic condition characterized by recurrent, unprovoked seizures,...
36
Seizures: Classification01:13

Seizures: Classification

Epilepsy is primarily characterized by unpredictable seizures, either provoked by an identifiable factor, such as injury or illness, or unprovoked, occurring spontaneously without apparent cause.
Seizures are typically classified into two main categories: focal and generalized seizures.
Focal Seizures
Focal seizures originate from specific regions of the brain. These seizures are further sub-classified into two types:
2.5K
Epilepsy ll: Types01:22

Epilepsy ll: Types

Recurrent seizures, stemming from abnormal electrical activity in the brain, are the defining characteristic of epilepsy, a chronic neurological condition. Because seizure features vary greatly, epilepsy is classified using two systems: by seizure type and by epilepsy syndromes. These classifications enable clinicians to describe seizure patterns and select suitable treatment strategies.I. Classification by Seizure Type1. Focal EpilepsyFocal epilepsy begins in one hemisphere of the brain.
35
Seizures ll: Types01:19

Seizures ll: Types

Seizures are sudden bursts of abnormal electrical discharge in the brain that interfere with normal function. They are commonly divided into three groups: focal seizures, generalized seizures, and other types that do not fit neatly into either category.Focal SeizuresFocal seizures begin in a single brain region. When awareness is preserved, they are called focal aware seizures and may cause sensations such as tingling, unusual smells, or flashing lights. When awareness is impaired, they are...
27
Epilepsy and Seizures: Overview01:24

Epilepsy and Seizures: Overview

Epilepsy is a chronic neurological disease marked by recurrent, unpredictable seizures. These seizures are caused by abnormal electrical discharges in the brain, leading to behavior, sensation, or consciousness alterations. They can also cause transient impairment of awareness, interfering with daily activities.
Various factors can trigger epilepsy, including genetic factors, brain damage, metabolic causes, and unknown etiology. Diagnosis of epilepsy involves electroencephalography (EEG), which...
1.7K