[Cardiac resynchronization in a patient with congenitally corrected transposition of the great arteries]
Pedro Alexandre Sousa1, Diogo Cavaco2, Pedro Adragão2
1Serviço de Cardiologia, Hospital de Faro, E.P.E., Faro, Portugal.
Insights
This study details the first reported case in Portugal of cardiac resynchronization therapy for congenitally corrected transposition of the great arteries. This rare heart defect treatment involved a 31-year-old woman with heart failure.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Electrophysiology
Background:
- Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital heart defect.
- ccTGA can lead to systemic ventricular dysfunction and conduction abnormalities.
- Cardiac resynchronization therapy (CRT) use in congenital heart disease is not well-established.
Observation:
- A 31-year-old woman with ccTGA, heart failure, and a history of two cardiac surgeries presented with a DDDR pacemaker.
- The patient underwent successful transvenous CRT implantation.
- This represents the first reported case of transvenous CRT in a ccTGA patient in Portugal.
Findings:
- Successful implantation and likely clinical benefit of CRT in a complex ccTGA case.
- Demonstrates the feasibility of transvenous CRT in patients with ccTGA and heart failure.
- Highlights the importance of exploring advanced pacing strategies for challenging congenital heart conditions.
Implications:
- CRT may be a viable therapeutic option for select patients with ccTGA and heart failure.
- This case expands the understanding of CRT application in adult congenital heart disease.
- Further research is warranted to establish CRT guidelines for ccTGA patients.
Abstract:
Congenitally corrected transposition of the great arteries is a rare heart defect that can be associated with systemic ventricular dysfunction and conduction disturbances. The use of cardiac resynchronization therapy in patients with congenital heart disease is not fully established. The authors report a case of cardiac resynchronization therapy in a 31-year-old woman with a history of congenitally corrected transposition of the great arteries and heart failure, who had undergone two heart surgeries and had a DDDR pacemaker implanted. To our knowledge this is the first case reported in Portugal of cardiac resynchronization therapy by transvenous access in a patient with congenitally corrected transposition of the great arteries.
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