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Cotrel-Dubousset instrumentation in neurofibromatosis spinal problems
1Department of Orthopedic Surgery, Miami Children's Hospital, Florida.
Clinical Orthopaedics and Related Research
|August 1, 1989
Summary
Cotrel-Dubousset (CD) instrumentation effectively treats spinal deformities in neurofibromatosis patients. This surgical approach achieved significant correction and fusion, even in complex cases, avoiding complications like pseudoarthrosis.
Area of Science:
- Orthopedic Surgery
- Spinal Deformity Correction
- Neurofibromatosis Research
Background:
- Neurofibromatosis is associated with various spinal deformities, including scoliosis and kyphoscoliosis.
- Surgical management of these complex spinal abnormalities presents significant challenges.
Purpose of the Study:
- To evaluate the efficacy of Cotrel-Dubousset (CD) instrumentation in surgically managing spinal deformities in patients with neurofibromatosis.
- To assess the outcomes of CD instrumentation in different types of neurofibromatosis-related spinal conditions.
Main Methods:
- Retrospective analysis of 12 neurofibromatosis patients with spinal deformities treated with CD instrumentation.
- Inclusion of patients with regular scoliosis, dysplastic kyphoscoliosis, and post-laminectomy spinal instability.
- Average follow-up period of 33 months.
Main Results:
- Significant frontal correction (average 69%) and axial derotation (average 33%) in regular scoliosis cases.
- Restoration of sagittal normalcy without external immobilization or pseudoarthrosis in scoliosis patients.
- Successful arthrodesis achieved in a complex dysplastic kyphoscoliosis case with combined anterior and posterior instrumentation.
- Stabilization and fusion achieved in a patient with multilevel thoracic laminectomy without immobilization.
Conclusions:
- Cotrel-Dubousset instrumentation is an effective surgical option for neurofibromatosis-associated spinal deformities.
- The technique demonstrates versatility in addressing various complex spinal conditions, including scoliosis, kyphoscoliosis, and post-laminectomy instability.
- CD instrumentation facilitates successful fusion and correction while minimizing the need for prolonged immobilization.