[The current classification of systemic vasculitides]

Area of Science:

• Rheumatology
• Immunology
• Pathology

Context:

• Systemic vasculitides (SV) are severe, multiorgan diseases impacting patient prognosis.
• Accurate classification is crucial for timely diagnosis and effective treatment of SV.
• The 2012 International Consensus Conference revised SV nomenclature.

Purpose:

• To present the revised nomenclature and definitions of major systemic vasculitis forms.
• To incorporate current trends and understanding of SV pathogenesis and clinical features.
• To improve the classification system for systemic vasculitides.

Summary:

• The 2012 International Consensus Conference on the Nomenclature of Systemic Vasculitis revised existing classifications.
• New categories of vasculitis were added based on contemporary clinical and pathogenetic insights.
• Definitions were updated to reflect current understanding and practical application in diagnosing SV.

Impact:

• A refined classification system can reduce diagnostic errors in systemic vasculitis.
• Improved nomenclature facilitates better communication and understanding among clinicians.
• Enhanced classification supports more accurate prognostication and tailored treatment strategies for SV patients.