Budd-Chiari syndrome: treatment with percutaneous transhepatic recanalization and dilation

Area of Science:

• Vascular Surgery
• Pediatric Gastroenterology
• Interventional Radiology

Background:

• Budd-Chiari syndrome in children is rare and often linked to venous obstruction.
• Membranous obstruction of hepatic veins and inferior vena cava webs are specific etiologies.
• Timely diagnosis and intervention are crucial for managing pediatric Budd-Chiari syndrome.

Observation:

• A pediatric patient presented with Budd-Chiari syndrome.
• Imaging revealed membranous obstruction of hepatic veins and an inferior vena cava web.
• Clinical manifestations included hepatomegaly and ascites.

Findings:

• Transhepatic catheter venography confirmed the venous occlusive disease.
• Percutaneous transhepatic recanalization and balloon dilation were performed.
• Successful recanalization of the hepatic veins and inferior vena cava was achieved.

Implications:

• Percutaneous intervention offers a minimally invasive treatment option for pediatric Budd-Chiari syndrome.
• Successful recanalization can rapidly alleviate symptoms like hepatomegaly and ascites.
• This approach can normalize coagulation parameters, improving patient outcomes.