Anatomically corrected malposition of the great arteries: two case reports
Erkut Oztürk1, Ender Odemiş2, Oykü Tosun2
1Department of Pediatric Cardiology, Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, İstanbul, Turkey. erkut_ozturk@yahoo.com.
Insights
Anatomically corrected malposition of the great arteries (ACMGA) is a rare congenital heart defect where the aorta and pulmonary artery roots run parallel. Early diagnosis through echocardiography and other imaging is crucial for differentiating it from similar conditions.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Anatomically corrected malposition of the great arteries (ACMGA) is a rare congenital anomaly.
- It is characterized by parallel origins of the aorta and main pulmonary artery (PA) with normal ventriculoarterial connections.
- Distinguishing ACMGA from other great artery anomalies is clinically significant.
Observation:
- Two cases of ACMGA are presented: a 5-month-old boy and a 1-month-old girl.
- Echocardiography is the primary diagnostic tool.
- Advanced imaging like CT angiography and MRI may be necessary in complex cases.
Findings:
- ACMGA involves the aorta arising abnormally from the left ventricle and the PA from the right ventricle.
- The study highlights the diagnostic challenges and importance of differential diagnosis.
- Accurate identification is key to appropriate management.
Implications:
- This case series emphasizes the need for vigilance in diagnosing ACMGA.
- Understanding ACMGA aids in differentiating it from other great artery malpositions.
- Timely diagnosis impacts patient outcomes and treatment strategies for congenital heart defects.
Abstract:
Anatomically corrected malposition of the great arteries (ACMGA) is defined as parallel arising of aorta and main pulmonary artery (PA) roots although ventriculoarterial connection is normal. Abnormally related aorta arises from the left ventricle, while abnormally related PA arises from the right ventricle. It can be diagnosed with via echocardiography. In some cases, additional imaging modalities such as computerized tomographic angiography and magnetic resonance are required. In this article, we presented two cases of ACMGA, 5-month-old boy and 1-month-old girl. We wanted to point out the importance of differential diagnosis of other great artery anomalies from this rare pathology.
