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Ectopia cordis with a double outlet right ventricle, large ventricular septal defect, malposed great arteries and

Rabiya Malik1, Mark V Zilberman, Liwen Tang

  • 1Cardiovascular Center, Tufts Medical Center, Tufts University School of Medicine, Boston, Massachusetts.

Echocardiography (Mount Kisco, N.Y.)
|November 21, 2014
PubMed

Insights

Ectopia cordis is a rare congenital defect where the heart is outside the chest. Surgical correction is complex due to associated heart abnormalities, impacting survival rates.

Area of Science:

  • Cardiology
  • Congenital Abnormalities
  • Pediatric Surgery

Background:

  • Ectopia cordis is a rare congenital malformation involving heart displacement outside the thoracic cavity.
  • Early surgical correction is crucial for survival, but often complicated by co-existing defects.

Observation:

  • This case discusses ectopia cordis with complex intracardiac and extracardiac malformations.
  • Specific anomalies include double outlet right ventricle, large VSD, malposed great arteries, and left ventricular hypoplasia.

Findings:

  • The combination of these defects presents significant surgical challenges.
  • Left ventricular hypoplasia is a critical factor limiting surgical success.

Implications:

  • Understanding these complex pathologies is vital for surgical planning and improving outcomes.
  • Further research into managing complex ectopia cordis cases is warranted.

Keywords:
double outlet right ventricleectopia cordisleft ventricular hypoplasiamalposed great arteriespentalogy of Cantrellventricular septal defect

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