Tuberous sclerosis and cardiac tumors: new electrocardiographic finding in an infant

Insights

Cardiac rhabdomyomas, common in children with tuberous sclerosis, can cause ECG abnormalities. This case highlights a unique T-wave finding in an infant with tuberous sclerosis and cardiac rhabdomyomas, previously undescribed in this patient population.

Area of Science:

  • Pediatric Cardiology
  • Oncology
  • Genetics

Background:

  • Cardiac rhabdomyoma is the most common primary cardiac tumor in children.
  • It is frequently associated with tuberous sclerosis complex (TSC).
  • While often asymptomatic, cardiac rhabdomyomas can manifest with various electrocardiographic (ECG) abnormalities.

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