Recurrent bacterial meningitis in a child with mondini dysplasia

Eda Kepenekli-Kadayifci1, Ayşe Karaaslan1, Serkan Atıcı1

  • 1Department of Pediatrics, Division of Pediatric Infectious Diseases, Pendik Training and Research Hospital, Marmara University Medical Faculty, Mimar Sinan Cad No. 41, Fevzi Cakmak Mah, Ust kaynarca-Pendik, 34899 Istanbul, Turkey.

Case Reports in Pediatrics
|November 29, 2014
PubMed

Insights

Mondini dysplasia, a congenital ear abnormality, can lead to hearing loss and recurrent meningitis. Diagnosis via CT scan identified this condition in a child with recurrent meningitis and hearing loss.

Area of Science:

  • Otolaryngology
  • Neurology
  • Pediatrics

Background:

  • Mondini dysplasia is a congenital inner and middle ear malformation.
  • It can manifest with sensorineural hearing loss, cerebrospinal fluid (CSF) leakage, and recurrent bacterial meningitis (RBM).
  • Early diagnosis is critical for managing RBM and preventing complications.

Purpose of the Study:

  • To present a case of recurrent bacterial meningitis (RBM) in a pediatric patient.
  • To highlight the role of imaging in diagnosing the underlying cause of RBM.
  • To illustrate the association between Mondini dysplasia and RBM.

Main Methods:

  • Case presentation of a three-year-old boy with RBM and unilateral sensorineural hearing loss.
  • Diagnostic evaluation included computerized tomography (CT) of the temporal bone.
  • Clinical history and imaging findings were analyzed.

Main Results:

  • The patient presented with recurrent bacterial meningitis and unilateral sensorineural hearing loss.
  • CT scan revealed cystic malformation in the cochlea and vestibular dilatation.
  • These findings were consistent with Mondini dysplasia.

Conclusions:

  • Mondini dysplasia should be considered in the differential diagnosis of recurrent bacterial meningitis in children.
  • CT imaging of the temporal bone is essential for identifying inner ear malformations.
  • Timely diagnosis of Mondini dysplasia can aid in the management and prevention of meningitis recurrence.

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