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Intrathecal Application of a Fluorescent Dye for the Identification of Cerebrospinal Fluid Leaks in Cochlear Malformation
Published on: February 29, 2020
Recurrent bacterial meningitis in a child with mondini dysplasia
Eda Kepenekli-Kadayifci1, Ayşe Karaaslan1, Serkan Atıcı1
1Department of Pediatrics, Division of Pediatric Infectious Diseases, Pendik Training and Research Hospital, Marmara University Medical Faculty, Mimar Sinan Cad No. 41, Fevzi Cakmak Mah, Ust kaynarca-Pendik, 34899 Istanbul, Turkey.
Abstract:
Mondini dysplasia, also known as Mondini malformation, is a developmental abnormality of the inner and middle ears that can cause hearing loss, cerebrospinal fluid (CSF) leakage, and recurrent bacterial meningitis (RBM), which is defined as two or more episodes of meningitis separated by a period of convalescence and the complete resolution of all signs and symptoms. An accurate diagnosis of the underlying pathology is crucial to prevent further episodes from occurring. Herein, we present a three-year-old boy with RBM and unilateral sensorineural hearing loss. During the evaluation to determine the etiology of the RBM, cystic malformation in the cochlea and vestibular dilatation consistent with Mondini dysplasia were detected via computerized tomography (CT) of the temporal bone.
Insights
Mondini dysplasia, a congenital ear abnormality, can lead to hearing loss and recurrent meningitis. Diagnosis via CT scan identified this condition in a child with recurrent meningitis and hearing loss.
Area of Science:
- Otolaryngology
- Neurology
- Pediatrics
Background:
- Mondini dysplasia is a congenital inner and middle ear malformation.
- It can manifest with sensorineural hearing loss, cerebrospinal fluid (CSF) leakage, and recurrent bacterial meningitis (RBM).
- Early diagnosis is critical for managing RBM and preventing complications.
Purpose of the Study:
- To present a case of recurrent bacterial meningitis (RBM) in a pediatric patient.
- To highlight the role of imaging in diagnosing the underlying cause of RBM.
- To illustrate the association between Mondini dysplasia and RBM.
Main Methods:
- Case presentation of a three-year-old boy with RBM and unilateral sensorineural hearing loss.
- Diagnostic evaluation included computerized tomography (CT) of the temporal bone.
- Clinical history and imaging findings were analyzed.
Main Results:
- The patient presented with recurrent bacterial meningitis and unilateral sensorineural hearing loss.
- CT scan revealed cystic malformation in the cochlea and vestibular dilatation.
- These findings were consistent with Mondini dysplasia.
Conclusions:
- Mondini dysplasia should be considered in the differential diagnosis of recurrent bacterial meningitis in children.
- CT imaging of the temporal bone is essential for identifying inner ear malformations.
- Timely diagnosis of Mondini dysplasia can aid in the management and prevention of meningitis recurrence.
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