Spinal nerve root haemangioblastoma associated with reactive polycythemia
Eric K C Law1, Ryan K L Lee1, James F Griffith1
1Department of Imaging & Interventional Radiology, Prince of Wales Hospital, The Chinese University of Hong Kong, 30-32 Ngan Shing Street, Shatin, New Territories, Hong Kong.
Case Reports in Radiology
|November 29, 2014
Summary
This study reports a rare extramedullary spinal haemangioblastoma in an adult, associated with reactive polycythemia. Surgical debulking led to symptom resolution, including polycythemia.
Area of Science:
- Neurology
- Oncology
- Radiology
Background:
- Haemangioblastomas typically occur in the cerebellum or spinal cord.
- Extramedullary spinal canal is an unusual location for haemangioblastomas.
- Association with polycythemia at this site is not well-documented.
Purpose of the Study:
- To present a case of extramedullary spinal haemangioblastoma with reactive polycythemia.
- To detail the clinical, imaging, and histological findings.
- To discuss the management and outcome.
Main Methods:
- Radiography and computed tomography (CT) for initial assessment.
- Magnetic resonance imaging (MRI) for vascularity evaluation.
- CT-guided biopsy and surgical debulking.
- Histological examination of the resected tumor.
Main Results:
- A medium-sized, slow-growing extramedullary spinal tumor was identified.
- Prominent flow voids on MRI indicated hypervascularity.
- Tumor debulking was performed due to intraoperative bleeding.
- Histology confirmed haemangioblastoma.
- Postoperative resolution of back pain and polycythemia.
Conclusions:
- Extramedullary spinal haemangioblastoma can occur with reactive polycythemia.
- Multimodal imaging is crucial for diagnosis.
- Surgical debulking can be effective in managing these rare tumors.
- Complete resolution of symptoms is achievable.
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