Myxoid fibrosarcoma of the left atrium and ventricle in pregnancy

Myxoid fibrosarcoma is rare in adults, and presentation during pregnancy is extremely rare. We report a woman who presented at 20+1 weeks of gestation with a 1-month history of swollen legs, exertional dyspnea, and cough with frothy sputum. Dual-source computed tomography and transthoracic echocardiography showed a left atrial mass. The dead fetus was delivered by caesarean section. Two weeks later, she underwent resection of the intracardiac mass and mitral valve replacement. Histopathologic examination showed myxoid fibrosarcoma. The patient refused postoperative adjuvant chemotherapy and radiotherapy. After 1 year, she had no apparent complications, and echocardiography showed no evidence of recurrence.