Large hiatal hernia in infancy with right intrathoracic stomach along with left sided morgagni hernia

Uzma Saeed1, Naveed Mazhar1, Shahla Zameer1

  • 1Department of Radiology, Children Hospital, Pakistan Institute of Medical Sciences, Islamabad.

Insights

This study details a rare case of congenital diaphragmatic hernia in an infant, presenting a unique combination of right-sided hiatal hernia with intrathoracic stomach and a left-sided Morgagni hernia. Early diagnosis and treatment are crucial for congenital diaphragmatic hernia to improve outcomes.

Area of Science:

  • Pediatric Surgery
  • Thoracic Surgery
  • Medical Imaging

Background:

  • Congenital diaphragmatic hernia (CDH) is a common fetal anomaly affecting diaphragm development.
  • Morgagni hernias typically occur anteriorly on the right, while Bochdalek hernias are posterolateral on the left.
  • Hiatal hernias involve stomach herniation into the thoracic cavity, usually on the left.

Observation:

  • A rare case of an 18-month-old girl with a complex diaphragmatic hernia is presented.
  • The patient exhibited a large hiatal hernia with the stomach herniating into the right thoracic cavity.
  • Additionally, a left-sided Morgagni hernia was diagnosed concurrently.

Findings:

  • This case presents a reverse scenario to typical CDH presentations, with right-sided intrathoracic stomach and left-sided Morgagni hernia.
  • The combination of hiatal and Morgagni hernias in this configuration is exceptionally rare.
  • Diagnostic imaging confirmed the unusual anatomical arrangement.

Implications:

  • This case highlights the importance of considering atypical presentations of CDH.
  • Accurate and early diagnosis of complex diaphragmatic hernias is vital for timely surgical intervention.
  • Understanding rare CDH variations can improve surgical planning and patient management strategies.

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