[Optic nerve infarction in Sneddon's syndrome].
P Romera Romero1, A Monés Llivina1, A Blazquez Abisu1
1Departamento de Oftalmología, sección de neuroftalmología, Hospital Universitari Germans Trias i Pujol, Badalona, Barcelona, España.
Archivos De La Sociedad Espanola De Oftalmologia
|December 23, 2014
Summary
This case study details optic nerve infarction in Sneddon's syndrome, a rare vasculitis. It highlights a unique presentation of this condition, expanding our understanding of its potential manifestations.
Area of Science:
- Vascular Neurology
- Ophthalmology
- Rheumatology
Background:
- Sneddon's syndrome is a rare, non-inflammatory vasculopathy characterized by persistent livedo reticularis and recurrent ischemic cerebrovascular events.
- While neurological symptoms and retinal infarctions are known complications, optic nerve involvement is exceptionally rare.
Observation:
- A 26-year-old woman with a history of Raynaud's phenomenon and livedo reticularis presented with visual field defects, hypertension, hematuria, and headache.
- Ophthalmic examination revealed multiple retinal and optic nerve head infarcts in both eyes.
Findings:
- This case represents the first documented instance of Sneddon's syndrome presenting with optic nerve infarction.
- The patient's presentation underscores the diverse and potentially severe ocular manifestations of Sneddon's syndrome.
Implications:
- This finding expands the spectrum of Sneddon's syndrome, emphasizing the need for ophthalmologic evaluation in affected patients.
- Early recognition and management are crucial to prevent irreversible vision loss and systemic complications associated with this vasculitis.
Related Concept Videos
01:22Photoreceptors and Visual Pathways
11.3K
At the molecular level, visual signals trigger transformations in photopigment molecules, resulting in changes in the photoreceptor cell's membrane potential. The photon's energy level is denoted by its wavelength, with each specific wavelength of visible light associated with a distinct color. The spectral range of visible light, classified as electromagnetic radiation, spans from 380 to 720 nm. Electromagnetic radiation wavelengths exceeding 720 nm fall under the infrared category,...
11.3K
01:14Cranial Nerves: Types Part I
6.8K
Cranial nerves are responsible for transmitting motor and sensory information between the brain and various parts of the body. There are twelve pairs of cranial nerves, with the first six being essential in sensory perception, motor control, and autonomic functions related to the head and neck.
Olfactory Nerve (Cranial Nerve I)
The olfactory nerve, or cranial nerve I, is unique as it is purely sensory and dedicated to the sense of smell. This nerve originates in the olfactory epithelium of the...
Olfactory Nerve (Cranial Nerve I)
The olfactory nerve, or cranial nerve I, is unique as it is purely sensory and dedicated to the sense of smell. This nerve originates in the olfactory epithelium of the...
6.8K
01:20Anatomy of the Eyeball
12.2K
The eye is a spherical, hollow structure composed of three tissue layers. The outer layer — the fibrous tunic, comprises the sclera — a white structure — and the cornea, which is transparent. The sclera encompasses some of the ocular surface, most of which is not visible. However, the 'white of the eye' is distinctively visible in humans compared to other species. The cornea, a clear covering at the front of the eye, enables light penetration. The eye's middle...
12.2K
01:25Glaucoma: Overview
1.7K
Glaucoma is an eye condition characterized by increased intraocular pressure that damages the retina and optic nerve, leading to irreversible blindness if left untreated. The human eye has various components, including the cornea, iris, pupil, lens, and optic nerve. Aqueous humor is secreted by the epithelium of the ciliary body in the posterior chamber and flows through the trabecular meshwork and canal of Schlemm, maintaining normal intraocular pressure. The trabecular meshwork and the canal...
1.7K