Related Experiment Video
Updated: Apr 19, 2026

Cox-Maze IV Procedure Concomitant with Valvular Surgery In Situs Inversus Dextrocardia: A Single-Center Experience in China
Published on: February 11, 2022
Congenital aneurysm of the aortomitral intervalvular fibrosa
Dingchao He1, Pranava Sinha1, Laura Olivieri2
1Division of Cardiac Surgery, Children's National Medical Center, Washington, DC.
Insights
Congenital left ventricular outflow tract (LVOT) aneurysm and subaortic stenosis in a child were successfully treated with aneurysm plication, stenosis resection, and septal myectomy. This case highlights effective surgical management for complex pediatric cardiac defects.
Area of Science:
- Cardiovascular Surgery
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Congenital left ventricular outflow tract (LVOT) aneurysm, particularly of the intervalvular fibrosa, is a rare condition.
- Left ventricular outflow tract obstruction can occur secondary to other congenital cardiac anomalies or surgical repairs.
- Aortic coarctation is a common congenital heart defect requiring surgical intervention.
Observation:
- A 5-year-old boy presented with a congenital LVOT aneurysm, LVOT obstruction post-ventricular septal defect repair, and aortic coarctation.
- The patient exhibited complex cardiac anatomy requiring multi-stage surgical consideration.
Findings:
- Successful surgical management included plication of the LVOT aneurysm.
- Resection of fibrous subaortic stenosis and septal myectomy were performed to relieve obstruction.
- The combined surgical approach effectively addressed the multiple cardiac anomalies.
Implications:
- This case demonstrates the feasibility of surgical correction for complex congenital LVOT aneurysms and associated obstructions.
- Effective management strategies can improve outcomes for pediatric patients with intricate cardiac malformations.
- Further research into long-term outcomes for such complex repairs is warranted.
Abstract:
A 5-year-old boy was found to have a congenital left ventricular outflow tract (LVOT) aneurysm of the intervalvular fibrosa, LVOT obstruction after repair of a perimembranous ventricular septal defect, and aortic coarctation. The patient underwent successful plication of the aneurysm, resection of the fibrous subaortic stenosis, and septal myectomy.
More Related Videos
13:10Direct Re-implantation of Left Coronary Artery into the Aorta in Adults with Anomalous Origin of Left Coronary Artery from the Pulmonary Artery ALCAPA
Published on: April 24, 2017
11:20A Rodent Model of The Ross Operation: Syngeneic Pulmonary Artery Graft Implantation in A Systemic Position
Published on: April 1, 2022
Related Concept Videos
Mitral Stenosis I: Introduction
Mitral Valve Prolapse I: Introduction
Aneurysm I: Introduction
Mitral Regurgitation I: Introduction
Mitral Stenosis II: Clinical features and Diagnostic Tests
Mitral Stenosis III: Medical Management