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Adrenocortical carcinoma in a 3% years old girl with hetro-sexual precocity
Damte Shimelis1, Amezene Tadesse, Jacob Schneider
1Department of Pediatrics, Addis Ababa University.
Ethiopian Medical Journal
|January 16, 2015
Abstract:
Adrenocortical carcinoma is a rare neoplasm in children. Hetro-sexual precocious puberty could be the initial presentation of a rare adrenocortical neoplasm in the pediatric age group. Features of hetro-sexual precocious puberty in a girl should alert the possibility of such a rare disease. We report a rare case of adrenocortical carcinoma in a three years and six months old girl who presented with hetro-sexual precocious puberty of two years duration. Left adrenalectomy was done and histopathology revealed adrenocortical carcinoma.