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Congenital cystic pulmonary malformations in children: our experience with 19 patients

Atila Turkyilmaz1, Yener Aydin1, Ali Fuat Erdem2

  • 1Ataturk University, Faculty of Medicine, Department of Thoracic Surgery, Erzurum, Turkey.

The Eurasian Journal of Medicine
|January 23, 2015
PubMed

Insights

Congenital cystic pulmonary malformations (CPM) require surgical intervention. Surgical treatment of 19 pediatric patients with CPM demonstrated no operative mortality and a mean hospitalization of 6.9 days, highlighting the necessity of surgery for symptom improvement and diagnosis.

Area of Science:

  • Pediatric Surgery
  • Thoracic Surgery
  • Congenital Malformations

Background:

  • Congenital cystic pulmonary malformations (CPM) are rare but can cause significant respiratory issues.
  • These anomalies include bronchogenic cysts (BC), pulmonary sequestration (PS), congenital lobar emphysema (CLE), and congenital cystic adenomatoid malformations (CCAM).
  • Infants may experience life-threatening respiratory distress, while older children and adults can present with recurrent pneumonia.

Purpose of the Study:

  • To present surgical treatment experience with pediatric CPM patients.
  • To discuss findings in conjunction with existing literature.
  • To emphasize the role of surgery in managing CPM.

Main Methods:

  • Retrospective evaluation of 19 patients under 16 years old treated between 1995 and 2008.
  • Analysis included diagnoses, age, gender, symptoms, lesion location, surgical technique, hospitalization, complications, and outcomes.
  • All patients underwent surgical resection.

Main Results:

  • Diagnoses included BC (5), PS (6), CLE (4), CCAM Type I (3), and combined PS/CCAM (1).
  • No operative mortality was observed.
  • Mean postoperative hospitalization was 6.9 days (range 4-17 days).

Conclusions:

  • CPM, including CLE, CCAM, and PS, can cause severe respiratory distress in infants.
  • BC, CCAM, and PS often present with recurrent pneumonia in children and adults.
  • Surgery is crucial for alleviating severe symptoms, preventing fatal complications, and obtaining histopathological diagnoses.
Abstract

Keywords:
CongenitalCystic pulmonary malformationsDiagnosisSurgery

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