Adolescents and adults with congenital heart diseases in oman

Asim Al-Balushi1, Hamood Al-Kindi2, Hamood Al-Shuaili3

  • 1Department of Pediatric Cardiology, Royal Hospital, Muscat, Oman.

Oman Medical Journal
|April 2, 2015
PubMed

Insights

This study examined congenital heart disease (CHD) in Oman, finding simple forms are common but complex cases have shorter survival. A national registry is recommended for better CHD management and outcomes.

Area of Science:

  • Cardiology
  • Public Health
  • Pediatric Medicine

Background:

  • Congenital heart disease (CHD) represents a significant global health concern.
  • Understanding the epidemiology of CHD in specific populations is crucial for targeted interventions.

Purpose of the Study:

  • To investigate the spectrum, demographics, and mortality rates of congenital heart disease (CHD) in Omani adolescents and adults.
  • To analyze survival outcomes based on CHD type and patient demographics.

Main Methods:

  • Retrospective analysis of electronic health records from the Royal Hospital, Muscat.
  • Inclusion of patients aged 13 years and above diagnosed with CHD.
  • Kaplan-Meier survival analysis to assess in-hospital mortality.

Main Results:

  • 600 CHD patients identified; 24% were 18 years or younger, with a median age of 24.
  • Simple CHDs, particularly atrial and ventricular septal defects (62.8%), were most prevalent.
  • Patients with Tetralogy of Fallot and Fontan experienced shorter survival times compared to literature benchmarks.

Conclusions:

  • Oman's CHD population primarily consists of younger individuals with simpler heart defects.
  • Complex congenital heart lesions are associated with significantly reduced survival rates.
  • Establishing a national CHD data registry is essential for improving disease management and reducing mortality.
Abstract

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