A Tumour for which Surgery will do more harm than good: A Case Report of Fibrodysplasia Ossificans Progressiva
1Department of Orthopaedics and Trauma, University College Hospital, Ibadan.
Aims And Objectives:
This case report is aimed at increasing awareness of fibrodysplasia ossificans progressiva, emphasizing the cardinal features comprising congenital great toe abnormality, initial soft tissue masses, eventual heterotopic ossifications with progressive limitation of joint movements and at reiterating the need to avoid unnecessary and potentially harmful surgical procedures in these patients.
Patient And Method:
We present a case report of an 11-year-old girl with characteristic heterotopic ossifications and bilateral hallux valgi deformities with previous history of biopsies. Excision of right axillary bony masses caused deterioration in her shoulder movements.
Result:
The patient was not improved by the surgical procedure.
Conclusion:
Orthopaedic surgeons and other health care workers need to be aware of this condition and avoid potentially harmful procedures like biopsies, excisions and surgical releases in these patients.
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