Intrathoracic lymphangiomatosis mimicking lymphangioleiomyomatosis in a young woman
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D W Swank1, N G Hepper, K E Folkert
1Department of Laboratory Medicine, University of North Dakota, Minot.
Mayo Clinic Proceedings
|October 1, 1989
Abstract:
In this report, we describe a case of lymphangiomatosis that mimicked lymphangioleiomyomatosis in a 20-year-old woman. Lung biopsy specimens showed proliferation of anastomosing lymphatic channels in the visceral pleura and dilated peribronchiolar and septal lymphatic channels. During 8 years of follow-up, this process behaved like lymphangioleiomyomatosis with reticulonodular infiltrates and worsening obstructive and restrictive changes evident on pulmonary function tests.