Aortic root thrombosis with coronary embolization following neo-aortic reconstruction in a child with hypoplastic
Elizabeth A Mitchell1, Darren P Berman1, Patrick I McConnell1
1The Heart Center, Nationwide Children's Hospital, Columbus, OH, USA.
Insights
Hypoplastic left heart syndrome (HLHS) survivors face rare complications after stage 2 palliation. This case report details aortic root thrombosis extending to coronary arteries and its successful treatment.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Surgery
- Cardiovascular Research
Background:
- Hypoplastic left heart syndrome (HLHS) management has evolved, with increasing long-term survivors.
- Complications of HLHS surgical palliation are well-documented, with most occurring after stage 1.
- Post-stage 2 complications are less common but can be severe, relating to surgical procedures and altered physiology.
Abstract:
In the recent era, the diagnosis, treatment options, postoperative management and outcomes of infants born with hypoplastic left heart syndrome (HLHS) have undergone dramatic changes. As is the case with many other novel treatment modalities used for congenital heart diseases, data concerning the long-term outcomes and complications of the various strategies become gradually more available as the numbers of survivors grow. In general, complications of the three-stage surgical palliation used for HLHS tend to occur most commonly following the first-stage surgery. Post-stage 2 complications are substantially less common, and centre on the procedure itself and the unique physiology of the cavopulmonary connection. In the following case report, we describe a relatively rare adverse outcome that occurred following a stage 2 surgery in the form of native aortic root thrombosis extending to the coronary arteries. The selected methods of treatment used in the catheterization laboratory and later in the operating theatre, as well as its outcomes are described.
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