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A Chinese classic phenylketonuria manifested as autism

C H Chen1, K J Hsiao

  • 1Department of Psychiatry, Veterans' General Hospital, Taipei, Taiwan, Republic of China.

Insights

Autism-like symptoms in children may indicate phenylketonuria, a treatable metabolic disorder. Early investigation is crucial, particularly when newborn screening for metabolic diseases is unavailable.

Area of Science:

  • Biochemistry
  • Pediatrics
  • Genetics

Background:

  • Autism Spectrum Disorder (ASD) is a neurodevelopmental condition.
  • Phenylketonuria (PKU) is an inborn error of metabolism.
  • Neonatal screening for metabolic diseases is not universally established.

Observation:

  • A 12-year-old Chinese boy presented with symptoms initially diagnosed as infantile autism.
  • The patient's condition was later confirmed to be classic phenylketonuria during adolescence.

Findings:

  • Classic phenylketonuria can manifest with autism-like symptoms.
  • Delayed diagnosis of PKU can occur in the absence of established neonatal screening programs.

Implications:

  • Investigating phenylketonuria is recommended for children presenting with apparent autism.
  • This approach is particularly important in regions lacking comprehensive newborn metabolic disease screening.
  • Early diagnosis and management of PKU can prevent severe neurodevelopmental outcomes.

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