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Updated: Apr 12, 2026
06:04
Systematic Hearing Performance Evaluation Process for Adolescents with Cochlear Implantation at Early Ages
Published on: March 24, 2023
947
Cochlear Implants in Children Diagnosed with CHARGE Syndrome.
Carolina Costa Cardoso1, Michelle Sales de Meneses1, Isabella Monteiro de Castro Silva2
1Audiologist; Speech Therapy, University Center Federal District (UNIPLAN), Brasília/DF, Brazil.
International Archives of Otorhinolaryngology
|May 21, 2015
Summary
Cochlear implants (CI) significantly improved auditory and language skills in a child with CHARGE syndrome. The study highlights CI effectiveness for hearing rehabilitation and language development in this complex condition.
Area of Science:
- Audiology
- Genetics
- Developmental Pediatrics
Background:
- CHARGE association is a genetic disorder characterized by multiple congenital anomalies, including hearing loss.
- Early intervention and technological aids are crucial for managing developmental challenges in CHARGE syndrome.
Observation:
- A 7-year-old girl with CHARGE syndrome and severe sensorineural hearing loss was evaluated before and after unilateral cochlear implant (CI) surgery.
- Data included medical records, therapy logs, and video analysis focusing on auditory and language skill development.
Findings:
- Significant improvements were observed in auditory integration (IT-MAIS: 5% to 90%) and speech use (MUSS: 75% to 72.5%) post-CI.
- Auditory skills advanced from category 1 to 6, and language skills from category 1 to 3, demonstrating substantial progress.
Implications:
- Cochlear implantation is an effective technological resource for enhancing hearing and facilitating language acquisition in children with CHARGE syndrome.
- Individualized therapeutic approaches are essential due to the heterogeneity of CHARGE syndrome presentations and outcomes.
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