Osteofibrous dysplasia-like adamantinoma in a 3-month-old male infant: a case report
Halil Buldu1, Tuncay Centel2, Hale Kırımlıoğlu3
1Memorial Hospital, Department of Orthopedics and Traumatology, İstanbul, Turkey. halilb77@hotmail.com.
Insights
This report details the youngest infant diagnosed with osteofibrous dysplasia-like adamantinoma (OFDLA) of the lower leg. Surgical treatment resulted in a positive outcome with no relapse after three years.
Area of Science:
- Pediatric Orthopedics
- Skeletal Dysplasias
- Surgical Oncology
Background:
- Osteofibrous dysplasia-like adamantinoma (OFDLA) is a rare bone tumor.
- OFDLA can potentially transform into classical adamantinoma, suggesting a pre-malignant nature.
- Early diagnosis and treatment are crucial for managing OFDLA.
Abstract:
We report a case of a very rarely seen osteofibrous dysplasia-like adamantinoma (OFDLA) of the lower leg in a 3-month-old male infant, making it the youngest case in the literature. OFDLA is typically regarded as a benign lesion; however, due to its convertibility into classical adamantinoma, it is recommended to evaluate it as a pre-malignant lesion. After OFDLA diagnosis with biopsy, our case underwent surgical resection and reconstruction with a large allograft. Patient experienced good outcomes and did not experience any local relapse in the 3-year follow-up.
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